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KMID : 0942820040030020156
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Journal of Korean Brain Tumor Society
2004 Volume.3 No. 2 p.156 ~ p.159
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Atypical Teratoid/Rhabdoid Tumor in the Central Nervous System
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Han Seong-Rok
Yoon Sang-Won
Lee Gi-Taek
Son Moon-Jun
Joo Mee
Whang Choong-Jin
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Abstract
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Atypical teratoid/Rhabdoid tumors(AT/RT) are aggressive neoplasm that afflict infants and young children and are the new entity among malignant pediatric brain tumors. These tumors show similar histological and radiological features to primitive neuroectodermal tumor-medulloblastoma(PNET-MB). So, these tumors have been misdiagnosed previously as PNET-MB. Separation of these two tumor types is crucial. Because the prognosis of a patient with an AT/RT is worse than that of a PNET-MB despite aggressive surgical treatment with or without adjuvant chemotherapy and radiation therapy. Recently, we experience a 5-month girl with a primary intracranial AT/RT in the posterior fossa. We report the case with a special emphasis on the differential diagnosis from PENT-MB.
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KEYWORD
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Atypical teratoid/rhabdoid tumor, Primitive neuro ectodermal -tumor, Medulloblastoma
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